Decompressive surgery in a patient with hyperostosis corticalis generalisata for relief of cognitive disability and dysaesthesia

Mirjam Datema, Natasha M Appelman-Dijkstra, Stefan A Hoyng, Marco J T Verstegen, Radboud W Koot

Research output: Contribution to journal/periodicalArticleScientificpeer-review

Abstract

A 28-year-old man with genetically confirmed hyperostosis corticalis generalisata (Van Buchem disease) suffered from headache and progressive cognitive and sensibility disorders. Bone formation of the skull was ongoing, leading to narrowing of the intracranial space and foramen magnum. A large bilateral frontoparietal craniotomy and decompression of the foramen magnum resulted in almost complete relief of his symptoms. This is the first report on successful decompressive surgery as a treatment of cognitive impairment and dysaesthesia.

Original languageEnglish
Pages (from-to)1215-8; discussion 1219
JournalActa Neurochirurgica
Volume157
Issue number7
DOIs
Publication statusPublished - Jul 2015

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